PERSISTENT LEFT SUPERIOR VENA CAVA AND ITS ASSOCIATION WITH CONGENITAL HEART DISEASE: A CT ANGIOGRAPHY STUDY

MAK AFRIDI; S ILYAS; I HUSSAIN; HD WAZIR; A AHMAD; . SOHAIB; F ALI; MS KHAN

doi:10.54112/bcsrj.v2024i1.659

Authors

MAK AFRIDI Department of Paeds Cardiology, Peshawar Institute of Cardiology, Pakistan
S ILYAS Department of Paeds Cardiology, MTI, LRH, Peshawar, Pakistan
I HUSSAIN Department of Paeds Cardiology, Peshawar Institute of Cardiology, Pakistan
HD WAZIR Department of Paeds Cardiology, Peshawar Institute of Cardiology, Pakistan
A AHMAD Department of Paeds Cardiology, Peshawar Institute of Cardiology, Pakistan
. SOHAIB Department of Paeds Cardiology, Peshawar Institute of Cardiology, Pakistan
F ALI Department of Paeds Cardiology, Peshawar Institute of Cardiology, Pakistan
MS KHAN Department of Paeds Cardiology, Peshawar Institute of Cardiology, Pakistan

DOI:

https://doi.org/10.54112/bcsrj.v2024i1.659

Keywords:

Persistent Left Superior Vena Cava, Congenital Heart Disease, CT Angiography, Vascular Anomaly

Abstract

Persistent Left Superior Vena Cava (PLSVC) is a common venous anomaly that is often associated with congenital heart disease (CHD) in pediatric patients. The significance of this anomaly lies in the potential complications that may arise during cardiac procedures. A prospective observational cohort study was conducted at the Peshawar Institute of Cardiology, a tertiary care heart facility in Peshawar, from January 2021 to January 2022. The study used CT angiography to assess the prevalence and characteristics of PLSVC in a cohort of 75 pediatric patients with CHD. The study also intended to provide valuable insights for preoperative planning and procedural success, addressing the challenges posed by PLSVC in the context of congenital heart anomalies. Demographic data, including age, gender, and clinical history, were collected for all 75 pediatric patients with CHD. CT angiography was used to identify PLSVC, and characteristics such as dimensions, trajectory, and drainage patterns were recorded. Data analysis involved descriptive statistics, chi-squared tests, and a significance level of p < 0.05. The study found that Tetralogy of Fallot (TOF) was the most prevalent CHD, constituting 26.7% of cases. The prevalence of PLSVC varied between males and females. Furthermore, the analysis of PLSVC drainage patterns demonstrated associations with specific types of CHD, providing a comprehensive understanding of the diverse manifestations of this anomaly. In conclusion, this study contributes valuable insights into the prevalence and characteristics of PLSVC in pediatric patients with CHD. The findings emphasize the importance of considering gender-specific and CHD-specific factors in medical interventions. These results have implications for clinical practice and future research in pediatric cardiology.

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