GENERAL ANESTHESIA IN A PATIENT WITH CHARCOT-MARIE-TOOTH DISEASE

S ISLAM; MNA KHAN; S MUSTAFA

doi:10.54112/bcsrj.v2023i1.401

Authors

S ISLAM Department of Anesthesia, Shifa International Hospital, Islamabad, Pakistan
MNA KHAN Department of Anesthesia, Shifa International Hospital, Islamabad, Pakistan
S MUSTAFA Department of Anesthesia, Shifa International Hospital, Islamabad, Pakistan

DOI:

https://doi.org/10.54112/bcsrj.v2023i1.401

Abstract

General anesthesia organization in patients with Charcot-Marie-Tooth Sickness (CMTD) presents novel moves and contemplations because of the hidden neuromuscular and fringe sensory system association. The main objective of the case report is to establish a safe general anesthesia protocol without triggering malignant hyperthermia in a patient with Charcot-Marie-Tooth disease. A 22-year-old female student presented to the plastic surgery department with a history of progressive bilateral foot drop (more on the left than right). She had been diagnosed with CMTD 10 years previously. No surgical procedure was done previously. There was no problem other than the foot drop. The patient was NKDA and NKFA allergic, and there was no medication previously. This case underscores the complexities of managing CMTD-related symptoms, particularly foot drop, in a young female patient. The multidisciplinary collaboration between plastic surgery, orthopedics, and Anesthesiology offers a holistic approach to improving mobility and enhancing the patient's quality of life through muscle-strengthening exercises and potential surgical interventions.

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